Molecular Classification
Protein aggregate
Other Names
Lewy bodies, Lewy neurites, Alpha-synuclein fibrils, Aggregated alpha-synuclein, SNCA aggregates
Disease Roles
Alpha-synuclein aggregate Overview
Alpha-synuclein aggregates are abnormal accumulations of the alpha-synuclein protein, primarily found in presynaptic terminals. These aggregates are central to the pathology of several neurodegenerative diseases, most notably Parkinson’s disease and other synucleinopathies. In its aggregated form, alpha-synuclein misfolds into β-sheet-rich fibrils that accumulate as Lewy bodies and Lewy neurites within neurons. These aggregates are considered a therapeutic target for disease modification.
Mechanism of Action
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Biological Functions
Neurotoxicity
Mitochondrial dysfunction
Oxidative stress
Apoptosis
Synaptic dysfunction
Disease Associations
Parkinson's Disease
Dementia with Lewy Bodies
Multiple System Atrophy
Synucleinopathies
Neurodegenerative disease
Safety Considerations
- Off-target effects
- Immune response
- Blood-brain barrier penetration
- Non-selective aggregate targeting
- Unintended consequences of disrupting protein homeostasis
Associated Biomarkers
Biomarker |
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Alpha-synuclein levels in cerebrospinal fluid |
Alpha-synuclein levels in blood |
Imaging of alpha-synuclein aggregates |